Osteopoikilosis in the ribs, pelvic region and spine: a case report

Мұқаба

Дәйексөз келтіру

Толық мәтін

Аннотация

Osteopoikilosis is a rare inherited benign bone dysplasia incidentally found on radiological exams. It is characterized by a specific radiological pattern: diffuse, round or oval, symmetrically shaped sclerotic bone areas distributed throughout the skeleton. It is essential to do a correct diagnosis because these lesions could be easily confused with bone metastasis.

We reported a case of an osteopoikilosis patient presenting to our clinic with transient loss of consciousness and without any numbness, tingling and weakness in the legs or other parts of the body. The computed tomography scan showed multiple small sclerotic foci bone islands, scattered throughout the thoracic and lumbar spine, ribs, pelvic bone, sacrum and bilateral proximal femur. No significant increase in the activity was detected in technetium-99m whole-body bone scintigraphy. The patient was diagnosed with characteristic radiological findings of osteopoikilosis and was followed up.

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Авторлар туралы

Maria Paparella

Department of Clinical and Experimental Medicine, Foggia University School of Medicine

Email: mt.paparella@gmail.com
ORCID iD: 0000-0003-2573-9509

MD

Италия, Viale L. Pinto 1, 71121, Foggia

Ilaria Gangai

Department of Clinical and Experimental Medicine, Foggia University School of Medicine

Email: hilary_ps@libero.it
ORCID iD: 0000-0001-9594-4810

MD

Италия, Viale L. Pinto 1, 71121, Foggia

Chiara Porro

Department of Clinical and Experimental Medicine, Foggia University School of Medicine

Email: chiara.porro@unifg.it
ORCID iD: 0000-0002-7526-6968

MD

Италия, Viale L. Pinto 1, 71121, Foggia

Laura Eusebi

Radiology Unit, Carlo Urbani

Email: lauraeu@virgilio.it
ORCID iD: 0000-0002-4172-5126

MD

Италия, Jesi

Ferdinando Silveri

Rheumatology Unit, University of Ancona

Email: fsilveri@libero.it
ORCID iD: 0000-0002-7847-245X

MD

Италия, Ancona

Aldo Cammarota

IRCCS-CROB

Email: aldo.cammarota@crob.it
ORCID iD: 0000-0003-4211-5140

MD

Италия, Rionero in Vulture

Giuseppe Guglielmi

Department of Clinical and Experimental Medicine, Foggia University School of Medicine; Radiology Unit, Barletta University Hospital

Хат алмасуға жауапты Автор.
Email: giuseppe.guglielmi@unifg.it
ORCID iD: 0000-0002-4325-8330

MD, Professor

Италия, Viale L. Pinto 1, 71121 Foggia; Foggia

Әдебиет тізімі

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© Paparella M.T., Gangai I., Porro C., Eusebi L., Silveri F., Cammarota A., Guglielmi G., 2022

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