Clinical case of fulminant course of atypical hemolytic-uremic syndrome
- Authors: Rysev G.A.1, Rysev A.V.1,2, Karyagina E.V.3, Medvedeva N.V.4, Mazurov V.I.2
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Affiliations:
- Saint Petersburg Research Institute of Emergency Medicine named after. I.I. Dzhanelidze
- North-Western State Medical University named after I.I. Mechnikov
- Saint Petersburg City Clinical Hospital No. 15
- Saint Petersburg City Oncohematology Center, City Clinical Hospital No. 31
- Issue: Vol 15, No 3 (2023)
- Pages: 85-90
- Section: Case report
- URL: https://journals.rcsi.science/vszgmu/article/view/249460
- DOI: https://doi.org/10.17816/mechnikov114815
- ID: 249460
Cite item
Abstract
This clinical observation describes a case of a fulminant course of an atypical hemolytic-uremic syndrome. The initial stage of the course of the disease is of particular interest, which was not accompanied by typical manifestations of atypical hemolytic-uremic syndrome according to the type of acquired autoimmune hemolytic anemia. Thus, revealing this clinical observation may help in the diagnosis of atypical hemolytic-uremic syndrome with atypical initial manifestations and avoid errors, delays and adverse outcomes of this disease.
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##article.viewOnOriginalSite##About the authors
Georgy A. Rysev
Saint Petersburg Research Institute of Emergency Medicine named after. I.I. Dzhanelidze
Author for correspondence.
Email: rysevszgmu@inbox.ru
SPIN-code: 1966-3919
Russian Federation, Saint Petersburg
Alexander V. Rysev
Saint Petersburg Research Institute of Emergency Medicine named after. I.I. Dzhanelidze; North-Western State Medical University named after I.I. Mechnikov
Email: 79213221618@yandex.ru
SPIN-code: 7715-0455
MD, Cand. Sci. (Med.), Assistant Professor
Russian Federation, Saint Petersburg; Saint PetersburgElena V. Karyagina
Saint Petersburg City Clinical Hospital No. 15
Email: rysevszgmu@inbox.ru
SPIN-code: 8158-0620
MD, Cand. Sci. (Med.)
Russian Federation, Saint PetersburgNadezhda V. Medvedeva
Saint Petersburg City Oncohematology Center, City Clinical Hospital No. 31
Email: or@hpmp.ru
MD, Cand. Sci. (Med.)
Russian Federation, Saint PetersburgVadim I. Mazurov
North-Western State Medical University named after I.I. Mechnikov
Email: maz.nwgmu@yandex.ru
ORCID iD: 0000-0002-0797-2051
SPIN-code: 6823-5482
MD, Dr. Sci. (Med.), Professor, Academician of the RAS, Honored Scientist of the Russian Federation
Russian Federation, Saint PetersburgReferences
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- Laurence J, Haller H, Mannucci PM, et al. Atypical hemolytic uremic syndrome (aHUS): essential aspects of an accurate diagnosis. Clin Adv Hematol Oncol. 2016;14 Suppl 11(11):2–15.
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