电邮这篇文章 青少年遗传性红斑性肢痛症。 一名青少年罕见疾病的临床观察
- 作者: Toriya V.G.1, Savina M.V.1, Vissarionov S.V.1, Baindurashvili A.G.1
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隶属关系:
- H. Turner National Medical Research Center for Сhildren’s Orthopedics and Trauma Surgery
- 期: 卷 10, 编号 1 (2022)
- 页面: 85-92
- 栏目: Clinical cases
- URL: https://journals.rcsi.science/turner/article/view/90396
- DOI: https://doi.org/10.17816/PTORS90396
- ID: 90396
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详细
论证。红斑性肢痛症是一种严重的慢性进行性疾病，有发作期和缓解期。该疾病的特征是有三重症状：四肢发红、局部皮肤温度升高和明显的神经性疼痛综合征。国内作者的少数研究介绍了关于红斑性肢痛症的数据，特别是在儿童中。这些出版物的性质是描述临床观察，评估患者在慢性疾病恶化期间住院时的皮肤表现和手术护理方面的疾病临床情况。
临床观察。本文讨论了一例15岁青少年遗传性红斑性肢痛症的临床病例，详细描述了疾病的病程，从最初的表现开始。
讨论。三年半以来，尽管早期诊断并坚持药物治疗，包括非甾体抗炎药、抗抑郁药、抗惊厥药、抗组胺药、阿片类药物、激素治疗、外用利多卡因和银质软膏，但该疾病进展缓慢，对治疗产生了耐受性疼痛综合征，有发作期和不完全缓解期。
结论。临床观察表明，本病病程为慢性、难治性。鉴于对这种疾病的明确病因缺乏了解，而且表现形式多样，对红斑性肢痛症患者应采取多学科治疗方法，寻求新的治疗方法，包括使用神经外科技术治疗慢性疼痛。
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作者简介
Vachtang G. Toriya
H. Turner National Medical Research Center for Сhildren’s Orthopedics and Trauma Surgery
编辑信件的主要联系方式.
Email: vakdiss@yandex.ru
ORCID iD: 0000-0002-2056-9726
SPIN 代码: 1797-5031
MD, Neurosurgeon
俄罗斯联邦, Saint PetersburgMargarita V. Savina
H. Turner National Medical Research Center for Сhildren’s Orthopedics and Trauma Surgery
Email: drevma@yandex.ru
ORCID iD: 0000-0001-8225-3885
SPIN 代码: 5710-4790
Scopus 作者 ID: 57193277614
MD, PhD, Cand. Sci. (Med.)
俄罗斯联邦, Saint PetersburgSergei V. Vissarionov
H. Turner National Medical Research Center for Сhildren’s Orthopedics and Trauma Surgery
Email: vissarionovs@gmail.com
ORCID iD: 0000-0003-4235-5048
SPIN 代码: 7125-4930
Scopus 作者 ID: 6504128319
Researcher ID: P-8596-2015
MD, PhD, Dr. Sci. (Med.), Professor, Corresponding Member of RAS
俄罗斯联邦, Saint PetersburgAlexey G. Baindurashvili
H. Turner National Medical Research Center for Сhildren’s Orthopedics and Trauma Surgery
Email: turner011@mail.ru
ORCID iD: 0000-0001-8123-6944
SPIN 代码: 2153-9050
Scopus 作者 ID: 6603212551
MD, PhD, Dr. Sci. (Med.), Professor, Member of RAS, Honored Doctor of the Russian Federation
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