“Superior Pectus Carinatum” (Currarino–Silverman Syndrome) in a 66-year-old woman: a case report
- Autores: Mannatrizio D.1, Fascia G.1, Guglielmi G.1,2
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Afiliações:
- Department of Clinical and Experimental Medicine, Foggia University School of Medicine
- Radiology Unit, Barletta University Hospital
- Edição: Volume 3, Nº 2 (2022)
- Páginas: 141-148
- Seção: Case reports
- URL: https://journals.rcsi.science/DD/article/view/104865
- DOI: https://doi.org/10.17816/DD104865
- ID: 104865
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Resumo
The premature fusion of some of the sternal ossification centers and the obliteration of the manubrio-sternal joint caused a rare deformity called Currarino–Silverman syndrome. Patients present an abnormally short sternum with a forward angulation at the manubrio-sternal junction. Cardiopulmonary diseases and spinal deformities are the most frequent related disorders. It was also described as a component of Turner’s and Noonan’s syndromes.
Herein, we present the case of a 66-year-old woman who presented to our clinic for follow-up computed tomography after surgery and chemotherapy for breast cancer with frequent episodes of dyspnea, wheezing, bronchitis, and mild dyspnea annually, which was more frequent during childhood. Computed tomography showed the absence of metastatic lesions and other accompanying diseases, except for a rare deformity of the anterior chest wall, the so-called, a “superior” pectus carinatum, a chondromanubrial deformity with a dorsal-open angle of 130º, and a sternum body length of 9 cm, which is not depressed in the lower third.
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##article.viewOnOriginalSite##Sobre autores
Domenico Mannatrizio
Department of Clinical and Experimental Medicine, Foggia University School of Medicine
Email: dr.mannatrizio@gmail.com
ORCID ID: 0000-0003-3365-7132
MD
Itália, FoggiaGiacomo Fascia
Department of Clinical and Experimental Medicine, Foggia University School of Medicine
Email: giacomo.fascia@unifg.it
ORCID ID: 0000-0001-5244-5093
MD
Itália, FoggiaGiuseppe Guglielmi
Department of Clinical and Experimental Medicine, Foggia University School of Medicine; Radiology Unit, Barletta University Hospital
Autor responsável pela correspondência
Email: giuseppe.guglielmi@unifg.it
ORCID ID: 0000-0002-4325-8330
MD, Professor
Itália, Foggia; BarlettaBibliografia
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