The experience of using a modern mixture for oral nutrition in a child with epidermolysis bullosa

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  • Authors: Erpuleva Y.V.1,2, Shurova L.V.1,3, Dmitrienko L.I.1
  • Affiliations:
    1. State Budgetary Healthcare Institution of Moscow “Speranskiy Children’s City Clinical Hospital № 9 of Moscow Department of Health”
    2. Federal State Autonomous Educational Institution of Higher Education “I.M. Sechenov First Moscow State Medical University” of the Ministry of Education of Russia (Sechenov University)
    3. Federal State Autonomous Educational Institution of Higher Education “Pirogov Russian National Research Medical University” of the Ministry of Education of Russia
  • Issue: Vol 1, No 1 (2020)
  • Pages: 47-51
  • Section: Case reports
  • URL: https://journals.rcsi.science/2658-4433/article/view/20703
  • DOI: https://doi.org/10.17816/clinutr20703
  • ID: 20703

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Abstract

Bullous epidermolysis is a congenital disease characterized by skin vulnerability due to the formation of blisters and erosion on the skin and mucous membranes, which makes it difficult for a child to eat naturally. The problem of providing the necessary nutrients to children with this serious illness remains relevant. The article shows its own clinical experience in the use of modern enteral nutritional mixtures in a child with epidermolysis bullosa. Given the skin manifestations, the possibility of infection of the catheter for prolonged parenteral nutrition, children with bullous epidermolysis are not recommended for prolonged use of parenteral nutrition, so the use of modern mixtures for enteral nutrition remains the method of choice.

About the authors

Yu. V. Erpuleva

State Budgetary Healthcare Institution of Moscow “Speranskiy Children’s City Clinical Hospital № 9 of Moscow Department of Health”; Federal State Autonomous Educational Institution of Higher Education “I.M. Sechenov First Moscow State Medical
University” of the Ministry of Education of Russia (Sechenov University)

Author for correspondence.
Email: j_stier@mail.ru
ORCID iD: 0000-0002-8018-3366

д.м.н., врач-педиатр

Russian Federation, Мoscow

L. V. Shurova

State Budgetary Healthcare Institution of Moscow “Speranskiy Children’s City Clinical Hospital № 9 of Moscow Department of Health”; Federal State Autonomous Educational Institution of Higher Education “Pirogov Russian National Research Medical University” of the Ministry of Education of Russia

Email: shuroval@mail.ru

врач-хирург ДКБ № 9 им. Г. Н. Сперанского

Russian Federation, Moscow

L. I. Dmitrienko

State Budgetary Healthcare Institution of Moscow “Speranskiy Children’s City Clinical Hospital № 9 of Moscow Department of Health”

Email: dgkb9@zdrav.mos.ru

врач-диетолог ДКБ № 9 им. Г. Н. Сперанского

Russian Federation, Мoscow

References

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Copyright (c) 2020 Erpuleva Y.V., Shurova L.V., Dmitrienko L.I.

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