A rare case of systemic AL-amyloidosis under the mask of myocardial infarction in the absence of myocardial hypertrophy: case report
- 作者: Boldueva S.1, Evdokimov D.1, Rozhdestvenskaya M.2, Vinnichuk S.1, Mitrofanova L.3
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隶属关系:
- Mechnikov North-Western State Medical University
- LLC «AVA-PETER»
- Almazov National Medical Research Centre
- 期: 卷 13, 编号 2 (2022)
- 页面: 101-106
- 栏目: Case reports
- URL: https://journals.rcsi.science/2221-7185/article/view/120356
- DOI: https://doi.org/10.17816/CS105142
- ID: 120356
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Systemic amyloidosis is a group of diseases associated with extracellular deposition of fibrillar proteins, resulting in the loss of normal organ structure and function. AL-amyloidosis occurs when amyloid is deposited, consisting of full-length lambda or kappa immunoglobulin light chains, or fragments thereof. This article describes the complexity of timely diagnosis of systemic AL-amyloidosis with a predominant heart lesion in the absence of myocardial «hypertrophy» on the example of an elderly patient in whom the leading manifestation of the disease was heart failure with a preserved left ventricular ejection fraction.
作者简介
Svetlana Boldueva
Mechnikov North-Western State Medical University
Email: svetlanaboldueva@mail.ru
ORCID iD: 0000-0002-1898-084X
D. Sci. (Med.), Prof.
俄罗斯联邦, Saint PetersburgDmitriy Evdokimov
Mechnikov North-Western State Medical University
Email: kasabian244@gmail.com
ORCID iD: 0000-0002-3107-1691
Graduate Student
俄罗斯联邦, Saint PetersburgMarina Rozhdestvenskaya
LLC «AVA-PETER»
Email: samok-marina@yandex.ru
ORCID iD: 0000-0002-6298-547X
Cand. Sci. (Med.), Multidisciplinary Clinic «Scandinavia»
俄罗斯联邦, Saint PetersburgSergey Vinnichuk
Mechnikov North-Western State Medical University
Email: Sergei.Vinnichuk@szgmu.ru
ORCID iD: 0000-0002-9590-6678
Cand. Sci. (Med.)
俄罗斯联邦, Saint PetersburgLyubov Mitrofanova
Almazov National Medical Research Centre
编辑信件的主要联系方式.
Email: lubamitr@yandex.ru
ORCID iD: 0000-0003-0735-7822
D. Sci. (Med.), Assoc. Prof.
俄罗斯联邦, Saint Petersburg参考
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