Hepatopulmonary syndrome

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Abstract

Hepatopulmonary syndrome (HPS) is a frequent complication of terminal liver disease. The HPS is based on the development of pulmonary vascular dilatation in response to the increase in the concentration of circulating vasoactive substances. To diagnose with HPS, the triad of symptoms is required: liver disease and/or portal hypertension, pulmonary vascular dilatation, and hypoxemia. The main therapeutic measures in HPS are the oxygen therapy and orthotopic liver transplantation.

About the authors

S. N Avdeev

Scientific-Research Institute of Pulmonology

Email: serg_avdeev@list.ru
д-р мед. наук, проф., рук. клин. отд. ФГБУ НИИ пульмонологии 105077, Russian Federation, Moscow, ul. 11-ia Parkovaia, d. 32

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