Email this article Clinical and MRT analysis of different variants in the Konovalov-Wilson’s disease
- Authors: Zalyalova Z.A.1, Bogdanov E.i1
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Affiliations:
- Kazan State Medical University
- Issue: Vol XXXIV, No 1-2 (2002)
- Pages: 5-10
- Section: Original article
- URL: https://journals.rcsi.science/1027-4898/article/view/87500
- DOI: https://doi.org/10.17816/nb87500
- ID: 87500
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Abstract
Seven patients with Konovalov—Wilson’s disease are presented and also materials concerning clinical and MRT analysis of the disease different variants are given. Multiple neurologic manifestations correlate with characteristic MRT picture — hypointensive in T1-images and hyperintensive in T2-images and there are foci in basal ganglia, thalamus and dentate nucleus in the form of «giant panda mouth», ventricle dilatation, diffuse, cerebral and cerebella atrophy. In akineticorigid syndrome absence of changes or slight ventricle dilatation are characteristic, in dystonia — bilateral hull damage; in intention tremor and dysmetria — atrophic or focal cerebellar changes.
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##article.viewOnOriginalSite##About the authors
Z. A. Zalyalova
Kazan State Medical University
Author for correspondence.
Email: info@eco-vector.com
Russian Federation, Kazan
E. i Bogdanov
Kazan State Medical University
Email: info@eco-vector.com
Russian Federation, Kazan
References
- Коновалов Н.В. Гепато-церебральная дистрофия. — М., 1960.
- Лекарь П.Г., Макарова В.А. Гепато-церебральная дистрофия. — Л., 1984.
- Alanen A., Komu М., Penttinen М. et al. // Br. J. Radiol. — 1999. - Vol. 72(860). — P.749—756.
- Brewer G.J., Yuzbasiyan-Gurkan V. // Medicine. — 1991. — Vol. 71. —P. 139—64.
- Dening T.R. // Int. J. Psychiatr. Med. — 1991. — Vol. 21. — P.135—48.
- Donfrid M., Jankovic G., Strahinja R. et al. // Hepatogastroenterology. — 1998. — Vol.45(23). — P.1774— 1776.
- Firneisz G., Szalay F., Halasz P. et al. // Acta Neurol. Scand. — 2000. — Vol. 101(4). — P. 286—288.
- Garnier H., Diederich N., Pilloy W. et al. // Rev. Neurol. — 1997. - Vol. 153(2). — P. 124—128. (Medline, abstact).
- Gow P.J., Peacock S.E., Chapman R.W. // J. Gastroenterol. Hepatol. — 2001. — Vol. 16(6). — P. 699—701.
- Hitoshi A., Ivata M., Yoshikawa K. // J. Neurol. Neurosurg. Psychiatry. — 1991. — Vol. 54. — P. 624—626.
- Horoupian D.S., Sternlieb I., Scheinberg I.H. // Clin. Neuropathol. — 1988. — Vbl.7. — P. 62—67.
- Huang C.C., Chu N.S. // Eur. Neurol. — 1998. — Vol. 39(1). — P.32—37.
- Imai N., Nozaki H., Miyata K. et al. // No To Shinkei. — 1999. — Medline, Abstract.
- Jones E.A., Weissenborn K. // J. Neurol. Neurosurg. and Psych. — 1997. — Vol.63. — P. 279—293.
- Kendall B.E., Pollock S.S., Bass N.M., Valentine L.S. // Neuroradiology. — 1981. — Vol.22. — P. 1—5.
- Kurzke J.F. Neuroepidemiology. In.: C. Braddley et al dds Neurology in Clinical Practice Vol. 1. Butterwarth-Heinemann. — 1996. — P. 673—686.
- Mochizuki H., Kamakura K., Masaki T. et al. // Neuroradiology. — 1997. —Vol. 39(3). — P.171—174.
- Oder W., Grimm G., Kollegger H., Ferenci P., Schneider B., Deecke L. // J. Neurol. — 1991. — Vol. 238. — P. 281—287.
- Roh J.K., Lee T.G., Wie B.A. et al. // Neurology. — 1994. — Vol 44.— P.1064—1068.
- Schilsy M.L. // Hepatology. — 1994. — Vol.20 — P. 529—533.
- Schwarz J., Antonini A., Kraft E. et al. // Neurology. — 1994. - Vol 44. — P.1079—1082.
- Sternlieb I., vanden Hamer C.J.A., Morell A.G. et al. // Gastroenterology. — 1973. — Vol. 64. — P. 99—105.
- Sternlieb I., Scheinberg I.H. Wilson’s disease. In: Millward-Sadler G.H., Wright R., Arthur M.J.P. eds. Wright’s liver and biliary disease. 3rd ed. Philadelphia: WB Saunders. — 1992. — P.965—975.
- Svetel M., Kozic D., Stefanova E. et al. // Mov. Disord. — 2001. — Vol. 16(4). —P. 719—723.
- Svetel M., Sternic N., Pejovic S., Kostic V.S. // Mov. Disord. — 2001. — Vol. 16(3). — P. 568—569.
