Email this article UTERUS AND VAGINAL APLASIA AND PELVIC KIDNEY - MANAGEMENT AND SURGICAL POSSIBILITY IN CONGENITAL ANOMALY CORRECTION
- Authors: Bobkova M.V1, Arakelyan A.S1, Kozachenko I.F1, Yarotskaya E.L1, Adamyan L.V1
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Affiliations:
- “The Academician V.I.Kulakov National Medical Research Center for Obstetrics, Gynecology and Perinatology”
- Issue: Vol 24, No 4 (2018)
- Pages: 220-224
- Section: Articles
- URL: https://journals.rcsi.science/0869-2106/article/view/38485
- DOI: https://doi.org/10.18821/0869-2106-2018-24-4-220-224
- ID: 38485
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Abstract
Objective. To clarify the possibilities and peculiarities of neovagival creation among the patients with MRKX syndrome and pelvic kidney. Subject and methods. Examination and surgical treatment were conducted in 3 patients with MRKX syndrome and pelvic kidney, including total laparoscopic colpopoiesis in 2 patients. Results. After surgical correction of vaginal and uterus aplasia in patiets with MRKX syndrome and pelvic kidney neovagina were created. In one patients neovagina were restore after previous surgery by vaginal approach because of extensive adhesions and high risk of laparoscopic surgery. In 2 patients - total laparoscopic colpopoiesis were perform without complications. Conclusion. Our clinical observations of surgical treatment in patients with MRKX syndrome and pelvic kidney shows possible surgical approaches of neovaginal creation depending of previous surgery and pelvic kidney localization, established during laparoscopy. Improvement of endoscopic technique and new modifications of neovaginal construction let us to increase the indications and possibilities of neovaginoplasty in patients with MRKX syndrome and pelvic kidney.
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##article.viewOnOriginalSite##About the authors
M. V Bobkova
“The Academician V.I.Kulakov National Medical Research Center for Obstetrics, Gynecology and Perinatology”117997, Moscow, Russian Federation
A. S Arakelyan
“The Academician V.I.Kulakov National Medical Research Center for Obstetrics, Gynecology and Perinatology”117997, Moscow, Russian Federation
I. F Kozachenko
“The Academician V.I.Kulakov National Medical Research Center for Obstetrics, Gynecology and Perinatology”117997, Moscow, Russian Federation
E. L Yarotskaya
“The Academician V.I.Kulakov National Medical Research Center for Obstetrics, Gynecology and Perinatology”117997, Moscow, Russian Federation
L. V Adamyan
“The Academician V.I.Kulakov National Medical Research Center for Obstetrics, Gynecology and Perinatology”117997, Moscow, Russian Federation
References
- Current evaluation of amenorrhea. Fertility and sterility. 2008; 90(5): Suppl.219-225.
- Herlin M., Bjorn A. M., Rasmussen M., Trolle B., Petersen M. B. Prevalence and patient characteristics of Mayer-Rokitansky-Kuster-Hauser syndrome: a nationwide registry-based study. Human reproduction. 2016; 31(10): 2384-90.
- Oppelt P., Renner S. P., Kellermann A., Brucker S., Hauser G. A., Ludwig K. S., Strissel P. L., Strick R., Wallwiener D., Beckmann M. W. Clinical aspects of Mayer-Rokitansky-Kuester-Hauser syndrome: recommendations for clinical diagnosis and staging. Human reproduction. - 2006; 21(3): 792-7.
- Sultan C., Biason-Lauber A., Philibert P. Mayer-Rokitansky-Kuster-Hauser syndrome: recent clinical and genetic findings. Gynecological endocrinology : the official journal of the International Society of Gynecological Endocrinology. 2009; 25(1): 8-11.
- Бобкова М. В., Баранова Е.Е., Адамян Л.В. Генетические аспекты формирования аплазии влагалища и матки: история изучения. Проблемы репродукции. 2015; 21(3): 10-15.
- Бобкова М. В., Баранова Е.Е., Кузнецова М.В., Трофимов Д.Ю., Адамян Л.В. Семейный случай синдрома Мейера-Рокитанского-Кюстер-Хаузера и обзор литературы.Проблемы репродукции. 2015; 21(4): 17-22.
- Vivante A., Kohl S., Hwang D. Y., Dworschak G. C., Hildebrandt F. Single-gene causes of congenital anomalies of the kidney and urinary tract (CAKUT) in humans. Pediatric nephrology. 2014; 29(4): 695-704
- Адамян Л. В., Кулаков В.И., Хашукоева А.З. Пороки развития матки и влагалища. Москва: «Медицина», 1998
- Oppelt P.G., Lermann J., Strick R., Dittrich R., Strissel P., Rettig I., Schulze C., Renner S. P., Beckmann M. W., Brucker S., Rall K., Mueller A. Malformations in a cohort of 284 women with Mayer-Rokitansky-Kuster-Hauser syndrome (MRKH). Reproductive biology and endocrinology: RB&E. 2012; 10: 57
- Fiaschetti V., Taglieri A., Gisone V., Coco I., Simonetti G. Mayer-Rokitansky-Kuster-Hauser syndrome diagnosed by magnetic resonance imaging. Role of imaging to identify and evaluate the uncommon variation in development of the female genital tract. Journal of radiology case reports. 2012; 6(4): 17-24.
- Lermann J., Mueller A., Wiesinger E., Haberle L., Brucker S., Wallwiener D., Dittrich R., Renner S.P., Beckmann M.W., Oppelt P.G. Comparison of different diagnostic procedures for the staging of malformations associated with Mayer-Rokitansky-Kuster-Hauser syndrome. Fertility and sterility. 2011; 96(1): 156-9.
- Rousset P., Raudrant D., Peyron N., Buy J. N., Valette P. J., Hoeffel C. Ultrasonography and MRI features of the Mayer-Rokitansky-Kuster-Hauser syndrome. Clinical radiology. 2013; 68(9): 945-52.
- Pompili G., Munari A., Franceschelli G., Flor N., Meroni R., Frontino G., Fedele L., Cornalba G. Magnetic resonance imaging in the preoperative assessment of Mayer-Rokitansky-Kuster-Hauser syndrome. La Radiologia medica. 2009; 114(5): 811-826.
- Адамян Л В., Панов В.О., Макиян З.Н., Панова М.М., Кулабухова Е. А. Магнитно-резонансная томография в дифференциальной диагностике аномалий развития матки и влагалища. Проблемы репродукции. 2009: 5: 14-27
- Hall-Craggs M.A., Williams C.E., Pattison S.H., Kirkham A.P., Creighton S.M. Mayer-Rokitansky-Kuster-Hauser syndrome: diagnosis with MR imaging. Radiology. 2013; 269(3): 787-92.
- Moriarty C.R., Miklos J.R., Moore R.D. Laparoscopic Davydov correction of a failed gracilis flap neovagina in a patient with Mayer-Rokitansky-Kuster-Hauser syndrome with a pelvic kidney. Journal of minimally invasive gynecology. 2013; 20(2): 262-5.
- Fedele L., Bianchi S., Dorta M., Zanconato G., Raffaelli R. Laparoscopic creation of a neovagina in women with pelvic kidney. The Journal of the American Association of Gynecologic Laparoscopists. 1999; 6(3): 327-9.
- Fedele L., Frontino G., Restelli E., Ciappina N., Motta F., Bianchi S. Creation of a neovagina by Davydov’s laparoscopic modified technique in patients with Rokitansky syndrome. American journal of obstetrics and gynecology. 2010; 202(1): 33 e31-36.
- Kerecuk L., Schreuder M. F., Woolf A. S. Renal tract malformations: perspectives for nephrologists. Nature clinical practice. Nephrology. 2008; 4(6): 312-25.
- Pellicano M., Penner I., Connola D., Cascone D., Sorrentino V., Gargano V., Masucci A., Stella N., Nappi C. [Voluminous ectopic polycystic ovaries in Mayer-Rokitansky-Kuster-Hauser syndrome]. Minerva ginecologica. 2005; 57(6): 655-8.
- Balci O., Karatayli R., Capar M. An incidental coexistence of Mayer-Rokitansky-Kuster-Hauser syndrome with pelvic ectopic kidney and perirenal endometrioma. Saudi medical journal. 2008; 29(9):1340-1.
- Friedler S., Grin L., Liberti G., Saar-Ryss B., Rabinson Y., Meltzer S. The reproductive potential of patients with Mayer-Rokitansky-Kuster-Hauser syndrome using gestational surrogacy: a systematic review. Reproductive biomedicine online. 2016; 32(1): 54-61.
- Liu X., Liu M., Hua K., Li B., Guo S. W. Sexuality after laparoscopic peritoneal vaginoplasty in women with Mayer-Rokitansky-Kuster-Hauser syndrome. Journal of minimally invasive gynecology. 2009; 16(6): 720-9.
- Zhou J. H., Sun J., Yang C. B., Xie Z. W., Shao W. Q., Jin H. M. Long-term outcomes of transvestibular vaginoplasty with pelvic peritoneum in 182 patients with Rokitansky’s syndrome. Fertility and sterility. 2010; 94(6): 2281-5.
- Bianchi S., Frontino G., Ciappina N., Restelli E., Fedele L. Creation of a neovagina in Rokitansky syndrome: comparison between two laparoscopic techniques. Fertility and sterility. 2011; 95(3): 1098-1100 e1091-3.
