Email this article A clinical case of isolated non-compact left ventricular myocardium in a 29-year-old patient
- Authors: Alieva A.M.1, Kovtyukh I.V.1, Teplova N.V.1, Voronkova K.V.1, Reznik E.V.1, Baykova I.E.1, Totolyan G.G.1, Timofeev V.T.1, Kotikova I.A.1, Nikitin I.G.1
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Affiliations:
- N.I. Pirogov Russian National Research Medical University
- Issue: Vol 30, No 3 (2024)
- Pages: 309-318
- Section: Case reports
- URL: https://journals.rcsi.science/0869-2106/article/view/262454
- DOI: https://doi.org/10.17816/medjrf627408
- ID: 262454
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Abstract
BACKGROUND: Non-compact left ventricular myocardium is a rare heterogeneous pathology, which in the two-layer structure of the myocardium. There is no generally accepted definition of this form of pathology for both echocardiography and cardiac magnetic resonance imaging. Non-compact left ventricular myocardium can occur at any age and is often asymptomatic. Treatment of non-compact left ventricular myocardium is nonspecific and symptomatic.
DESCRIPTION: This study describes a clinical case of a young patient who was diagnosed with non-compact left ventricular myocardium. The disease debuted in the form of cardiac arrhythmia. Holter monitoring showed frequent ventricular extrasystole and atrioventricular block of the first and second degrees. Moreover, echocardiography revealed a decrease in global contractile function of the left ventricle. The diagnosis was made after magnetic resonance imaging of the heart, which revealed the presence of non-compact myocardium of the anterior, lateral, and inferior walls of the left ventricle in the apical and middle segments. Sustained rhythm disturbances were not induced in electrophysiological research by rapid and programmed stimulation. The patient was prescribed antiarrhythmic therapy, followed by echocardiography Holter monitoring. In the future, the patient needs regular monitoring by a cardiologist.
CONCLUSION: Non-compact left ventricular myocardium should be diagnosed at an early stage, so that life expectancy can be increased owing to timely treatment of heart failure and the use of oral anticoagulants, antiarrhythmic drugs, cardiac resynchronization therapy, cardioverter-defibrillator implantation, and heart transplantation when other treatment options are ineffective.
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##article.viewOnOriginalSite##About the authors
Amina M. Alieva
N.I. Pirogov Russian National Research Medical University
Author for correspondence.
Email: amisha_alieva@mail.ru
ORCID iD: 0000-0001-5416-8579
SPIN-code: 2749-6427
MD, Cand. Sci. (Medicine), associate professor
Russian Federation, MoscowIrina V. Kovtyukh
N.I. Pirogov Russian National Research Medical University
Email: nurzhanna@yandex.ru
ORCID iD: 0000-0002-9176-1889
SPIN-code: 4746-3716
Russian Federation, Moscow
Natalia V. Teplova
N.I. Pirogov Russian National Research Medical University
Email: teplova.nv@yandex.ru
ORCID iD: 0000-0002-7181-4680
SPIN-code: 9056-1948
MD, Dr. Sci. (Medicine), professor
Russian Federation, MoscowKira V. Voronkova
N.I. Pirogov Russian National Research Medical University
Email: kiravoronkova@yandex.ru
ORCID iD: 0000-0003-1111-6378
SPIN-code: 1636-7627
MD, Dr. Sci. (Medicine), professor
Russian Federation, MoscowElena V. Reznik
N.I. Pirogov Russian National Research Medical University
Email: elenaresnik@gmail.com
ORCID iD: 0000-0001-7479-418X
SPIN-code: 3494-9080
ResearcherId: N-6856-2016
MD, Dr. Sci. (Medicine), professor
Russian Federation, MoscowIrina E. Baykova
N.I. Pirogov Russian National Research Medical University
Email: 1498553@mail.ru
ORCID iD: 0000-0003-0886-6290
SPIN-code: 3054-8884
MD, Cand. Sci. (Medicine), associate professor
Russian Federation, MoscowGayane G. Totolyan
N.I. Pirogov Russian National Research Medical University
Email: tgg03@mail.ru
ORCID iD: 0000-0002-9922-5845
SPIN-code: 1441-7740
MD, Cand. Sci. (Medicine), associate professor
Russian Federation, MoscowVitaliy T. Timofeev
N.I. Pirogov Russian National Research Medical University
Email: timofeev_vt@rsmu.ru
ORCID iD: 0000-0002-3805-5942
SPIN-code: 2323-5061
MD, Dr. Sci. (Medicine), associate professor
Russian Federation, MoscowIrina A. Kotikova
N.I. Pirogov Russian National Research Medical University
Email: kotikova.ia@mail.ru
ORCID iD: 0000-0001-5352-8499
SPIN-code: 1423-7300
Russian Federation, Moscow
Igor G. Nikitin
N.I. Pirogov Russian National Research Medical University
Email: igor.nikitin.64@mail.ru
ORCID iD: 0000-0003-1699-0881
SPIN-code: 3595-1990
MD, Dr. Sci. (Medicine), professor
Russian Federation, MoscowReferences
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