A patient with severe idiopathic pulmonary arterial hypertension: Is there a way out?


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Abstract

The paper considers a clinical example of current therapy for idiopathic pulmonary arterial hypertension in a female patient with its clinical deterioration. It shows the tactics of switching from one drug (bosentan) to others (macitentan) within in the same pathogenetic therapy group (endothelin receptor antagonists). The latest pulmonary hypertension classification (Nice, 2013) is presented. The current strategies of pathogenetic therapy for pulmonary hypertension are discussed.

About the authors

N A Tsareva

ФГБУ «НИИ пульмонологии» ФМБА России

Москва, Россия

S N Avdeev

ФГБУ «НИИ пульмонологии» ФМБА России

Москва, Россия

G V Neklyudova

ФГБУ «НИИ пульмонологии» ФМБА России

Москва, Россия

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