Пациент с тяжелым течением идиопатической легочной артериальной гипертензии: есть ли выход?


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Аннотация

Аннотация В статье рассматривается клинический пример современной терапии идиопатической легочной артериальной гипертензии у пациентки с клиническим ухудшением течения заболевания. Показана тактика замены одного препарата (бозентан) другим (мацитентан) в рамках одной группы патогенетической терапии (антагонисты рецепторов эндотелина). Представлена последняя классификация легочной гипертензии (Ницца, 2013 г.) Обсуждаются вопросы современной стратегии патогенетической терапии легочной гипертензии.

Об авторах

Н А Царева

ФГБУ «НИИ пульмонологии» ФМБА России

Москва, Россия

С Н Авдеев

ФГБУ «НИИ пульмонологии» ФМБА России

Москва, Россия

Г В Неклюдова

ФГБУ «НИИ пульмонологии» ФМБА России

Москва, Россия

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