Pathomorphological and clinical characteristics of blastic plasmocytoid dendritic cell neoplasm. Case report

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Abstract

The paper reveals the 5 cases date about blastic plasmacytoid dendritic cell neoplasm. The presented information demonstrates morphological, immunohistochemical data and clinical manifestations.

About the authors

Andrei A. Sherstnev

National Research Center for Hematology

Author for correspondence.
Email: sherstnevandrejj@mail.ru
ORCID iD: 0000-0002-1597-4591

аспирант патологоанатомического отд-ния, врач-стажер

Russian Federation, Moscow

Alla M. Kovrigina

National Research Center for Hematology

Email: sherstnevandrejj@mail.ru
ORCID iD: 0000-0002-1082-8659

д-р биол. наук, зав. патологоанатомическим отд-нием

Russian Federation, Moscow

Tatiana I. Solovyova

National Research Center for Hematology

Email: sherstnevandrejj@mail.ru
ORCID iD: 0000-0001-8246-6581

канд. мед. наук, врач-гематолог

Russian Federation, Moscow

Tatiana N. Moiseeva

National Research Center for Hematology

Email: sherstnevandrejj@mail.ru
ORCID iD: 0000-0001-9591-8508

канд. мед. наук, врач-гематолог, зав. отд-нием химиотерапии гематологических заболеваний с дневным стационаром

Russian Federation, Moscow

References

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  4. Trottier AM, Cerquozzi S, Owen CJ. Blastic plasmacytoid dendritic cell neoplasm: challenges and future prospects. Blood Lymphat Cancer. 2017;7:85-93. doi: 10.2147/BLCTT.S132060
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  15. Sukswai N, Aung PP, Yin CC, et al. Dual expression of TCF4 and CD123 is highly sensitive and specific for blastic plasmacytoid dendritic cell neoplasm. Am J Surg Pathol. 2019;43(10):1429-37. doi: 10.1097/PAS.0000000000001316
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Supplementary files

Supplementary Files
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2. Fig. 1. Observation 1. Lymph node biopsy. Blast tumor of plasmacytoid dendritic cells.

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3. Fig. 2. Observation 2. Skin lesion in a blast tumor from plasmacytoid dendritic cells.

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