Congenital lobar emphysema in 16-year-old girl: clinical observation

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Abstract

Congenital lobar emphysema is a rare variant of lung malformation, which is characterized by hyperinflation of one or more lobes, usually diagnosed in early childhood. In this article, we demonstrate a clinical case of asymptomatic middle lobe emphysema diagnosed in a 16-year-old girl.

About the authors

M. V. Samsonova

Research Institute of Pulmonology of the Federal Medical-Biological Agency of Russia

Author for correspondence.
Email: samary@mail.ru
ORCID iD: 0000-0001-8170-1260
SPIN-code: 9525-9085

Head of the Department

Russian Federation, 28, Orekchovy Boulevard, Moscow, 115682

K. Yu. Mikhaylichenko

Research Institute of Pulmonology of the Federal Medical-Biological Agency of Russia

Email: kirr.mih@gmail.com
ORCID iD: 0000-0002-9795-7022

науч. сотр. лаборатории патологической анатомии

Russian Federation, 28, Orekchovy Boulevard, Moscow, 115682 

A. L. Chernyayev

Research Institute of Pulmonology of the Federal Medical-Biological Agency of Russia; Research Institute of Human Morphology; Pirogov Russian National Research Medical University

Email: cheral12@gmail.com
ORCID iD: 0000-0003-0973-9250
SPIN-code: 4433-4567

докт. мед. на ук, профессор, заведующий отделом фундаментальной пульмонологии ФГБУ ФГБУ «НИИ пульмонологии» ФМБА России; ведущий научный сотрудник ФГБНУ «Научно-исследовательский институт морфологии человека»; профессор кафедры патологической анатомии и клинической патологической анатомии лечебного факультета ФГБОУ ВО «Российский национальный исследовательский медицинский университет имени Н.И. Пирогова» Минздрава России

Russian Federation, 28, Orekchovy Boulevard, Moscow, 115682; 3, Tsuryupy street, Moscow, 117418; 1, Ostrovityanova street, Moscow, 117997

A. V. Chernyak

Research Institute of Pulmonology of the Federal Medical-Biological Agency of Russia

Email: achi2000@mail.ru
ORCID iD: 0000-0002-2001-5504
SPIN-code: 9328-6440

канд. мед. наук, заведующий лабораторией функциональных и ультразвуковых методов исследования

Russian Federation, 28, Orekchovy Boulevard, Moscow, 115682

I. Ye. Tyurin

Russian Medical Academy of Continuous Professional Education

Email: igortyurin@gmail.com
ORCID iD: 0000-0003-3931-1431

докт. мед. наук, профессор, заведующий кафедрой рентгенологии и радиологии

Russian Federation, 2/1, Barrikadnaya st., Moscow, 125993

I. E. Stepanyan

Central TB Research Institute

Email: drstepanyan@mail.ru
ORCID iD: 0000-0002-2985-3379

докт. мед. наук, профессор, ведущий науч. сотр., советник директора

Russian Federation, 2, Yauzskaya Alley, Moscow, 107564

References

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Supplementary files

Supplementary Files
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1. JATS XML
2. Fig. 1. Perfusion lung scintigraphy: perfusion deficit in the right lung (front view)

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3. Fig. 2. Axial scan of CT scan of OGK hyperinflation of the middle lobe of the right lung, partial compression of the lower lobe, displacement of the mediastinum to the left

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4. Fig.3. Histological signs of the expansion of the alveolar passages and alveoli

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Copyright (c) 2018 Samsonova M.V., Mikhaylichenko K.Y., Chernyayev A.L., Chernyak A.V., Tyurin I.Y., Stepanyan I.E.

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This work is licensed under a Creative Commons Attribution-NonCommercial-ShareAlike 4.0 International License.

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