Epidemiology of hereditary diseases of the nervous system in the Republic of Tajikistan (by example of Hissar district)

The article presents epidemiological data concerning studies of hereditary diseases of the nervous system (HDNS) in the territory of Hissar district of Tajikistan. In total, 76 patients were identified (including 52 men and 24 women), and 9 different forms of HDNS were diagnosed. Among all forms, the most frequent form was limb-girdle muscular dystrophy (n=24), the prevalence of which was 8.4 per 100 000 population, which is 2.5 times higher than in districts of Khatlon region of the country. The lowest frequency was registered for Bekker progressive muscular dystrophy (n=1). The HDNS prevalence ratio between rural and urban areas was 1:1 (2.9 and 2.8 per 10 000 population, respectively). The total prevalence of HDNS all over the region was 28.8 per 100 000 population.