Idiopathic pulmonary fibrosis: from diagnosis to treatment

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Abstract

Idiopathic pulmonary fibrosis (IPF) is a severe progressive disease with a rapidly (for several years) onset fatal outcome. The disease occurs in the second half of life, the number of patients increases. In 2011, an official agreement between The American thoracic society and the European respiratory society was published, presenting a modern classification of idiopathic interstitial pneumonia. An important characteristic of the course of the disease is the nature of its progression. Allocate at least 3 options (phenotype) of the IPF. A special place within the IPF is worsening. The Russian respiratory society has established National recommendations for the diagnosis and treatment of patients with IPF, taking into account international agreements, the register of patients with IPF.

About the authors

E. I Shmelev

Central Research Institute of Tuberculosis

Email: eishmelev@mail.ru
д-р мед. наук, проф., зав. отд. дифференциальной диагностики туберкулеза легких 107564, Russian Federation, Moscow, Yauzskaia alleyia, d. 2

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