The difficult way in diagnostics of neurological manifestations of Sjogren's disease. Case report
- Authors: Shchepankevich M.S.1, Bogoderova L.A.2, Veretelnikov I.A.2, Taneeva E.V.2, Korobko D.S.1,2
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Affiliations:
- Novosibirsk State Medical University
- State Novosibirsk Regional Clinical Hospital
- Issue: Vol 25, No 11 (2023): Neurology and rheumatology
- Pages: 751-754
- Section: Articles
- URL: https://journals.rcsi.science/2075-1753/article/view/253988
- DOI: https://doi.org/10.26442/20751753.2023.11.202460
- ID: 253988
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Abstract
Sjogren's disease is an immunoinflammatory rheumatic disease that is characterized by damage to the secreting epithelial glands with the development of parenchymal sialadenitis with xerostomia and keratoconjunctivitis sicca with hypolacrymia. Due to the high heterogeneity of clinical manifestations of this disease, diagnosis is difficult. This article presents a clinical case of a patient with a detailed description of the manifestation, course, and treatment of Sjogren's disease with a rare combination of extraglandular complications in the form of polymyositis and secondary polyneuropathy.
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##article.viewOnOriginalSite##About the authors
Maria S. Shchepankevich
Novosibirsk State Medical University
Author for correspondence.
Email: mari.shchepankevich@mail.ru
ORCID iD: 0000-0001-5141-3292
Clinical Resident, Novosibirsk State Medical University
Russian Federation, NovosibirskLarisa A. Bogoderova
State Novosibirsk Regional Clinical Hospital
Email: mari.shchepankevich@mail.ru
ORCID iD: 0000-0002-2570-8035
Department Head, State Novosibirsk Regional Clinical Hospital
Russian Federation, NovosibirskIvan A. Veretelnikov
State Novosibirsk Regional Clinical Hospital
Email: mari.shchepankevich@mail.ru
ORCID iD: 0000-0002-8587-5679
Department Head, State Novosibirsk Regional Clinical Hospital
Russian Federation, NovosibirskElena V. Taneeva
State Novosibirsk Regional Clinical Hospital
Email: mari.shchepankevich@mail.ru
ORCID iD: 0000-0002-6538-6069
Service Head, State Novosibirsk Regional Clinical Hospital
Russian Federation, NovosibirskDenis S. Korobko
Novosibirsk State Medical University; State Novosibirsk Regional Clinical Hospital
Email: mari.shchepankevich@mail.ru
ORCID iD: 0000-0002-7938-3782
Cand. Sci. (Med.), Novosibirsk State Medical University; State Novosibirsk Regional Clinical Hospital
Russian Federation, Novosibirsk; NovosibirskReferences
- Панасюк Г.Д., Бобр Т.В. Болезнь Шегрена в практике врача: практическое пособие для врачей-офтальмологов. Гомель: РНПЦ РМиЭЧ, 2020 [Panasiuk GD, Bobr TV. Bolezn' Shegrena v praktike vracha: prakticheskoe posobie dlia vrachei-oftal'mologov. Gomel: RNPTs RMiECh, 2020 (in Russian)].
- Еловикова Т.М., Григорьев С.С. Сухой синдром (синдром Шегрена): проявления в полости рта: учебное пособие. Екатеринбург: ТИРАЖ, 2018 [Elovikova TM, Grigor'ev SS. Sukhoi sindrom (sindrom Shegrena): proiavleniia v polosti rta: uchebnoe posobie. Ekaterinburg: TIRAZh, 2018 (in Russian)].
- Сафонова Т.Н., Васильев В.И. Синдром Шегрена: руководство для врачей: М.: Московский государственный университет, 2013 [Safonova TN, Vasil'ev VI. Sindrom Shegrena: rukovodstvo dlia vrachei. Moscow: Moskovskii gosudarstvennyi universitet, 2013 (in Russian)].
- Shiboski CH, Shiboski SC, Seror R, et al. 2016 American College of Rheumatology/European League Against Rheumatism classification criteria for primary Sjogren’s syndrome: a consensus and data-driven methodology involving three international patient cohorts. Arthritis Rheumatol. 2017;69(1):35-45. doi: 10.1002/art.39859
- Alunno A, Carubbi F, Bartoloni E, et al. The kaleidoscope of neurological manifestations in primary Sjogren's syndrome. Clin Exp Rheumatol. 2019;118(3):192-8.
- Левин О.С. Полинейропатии. Клиническое руководство. М.: Медицинское информационное агентство, 2005 [Levin OS. Polineiropatii. Klinicheskoe rukovodstvo. Moscow: Meditsinskoe informatsionnoe agentstvo, 2005 (in Russian)].
- Koike H, Sobue G. Sjogren's syndrome-associated neuropathy. Brain Nerve. 2013;65(11):1333-42.
- Пирадов М.А., Супонева Н.А., Гришина Д.А. Полинейропатии: алгоритмы диагностики и лечения. М.: Горячая линия – телеком, 2020 [Piradov MA, Suponeva NA, Grishina DA. Polineiropatii: algoritmy diagnostiki i lecheniia. Moscow: Goriachaia liniia – telekom, 2020 (in Russian)].
- Liampas A, Parperis K, Erotocritou MF, et al. Primary Sjogren syndrome-related peripheral neuropathy: a systematic review and meta-analysis. Eur J Neurol. 2023;30(1):255-65. doi: 10.1111/ene.15555
- Ruiz-Lozano RE, Velazquez-Valenzuela F, Roman-Zamudio M, et al. Polymyositis and dermatomyositis: ocular manifestations and potential sight-threatening complications. Rheumatol Int. 2022;42(7):1119-31. doi: 10.1007/s00296-021-05035-7
- Seeliger T, Kramer E, Konen FF, et al. Sjogren's syndrome with and without neurological involvement. J Neurol. 2023;270(6):2987-96. doi: 10.1007/s00415-023-11613-5
- McCoy SS, Baer AN. Neurological complications of Sjogren’s syndrome: diagnosis and management. Curr Treatm Opt Rheumatol. 2017;3(4):275-88. doi: 10.1007/s40674-017-0076-9
- Baldini C, Pepe P, Quartuccio L, et al. Primary Sjogren’s syndrome as a multi-organ disease: impact of the serological profile on the clinical presentation of the disease in a large cohort of Italian patients. Rheumatology (Oxford). 2014;53:839-44. doi: 10.1093/rheumatology/ket427
- Rist S, Sellam J, Hachulla E, et al. Experience of intravenous immunoglobulin therapy in neuropathy associated with primary Sjogren's syndrome: a national multicentric retrospective study. Multicenter Study. Arthritis Care Res (Hoboken). 2011;63(9):1339-44. doi: 10.1002/acr.20495
- Blinova VG, Vasilyev VI, Rodionova EB, Zhdanov DD. The role of regulatory T Cells in the onset and progression of primary Sjogren’s syndrome. Cells. 2023;12(10):1359. doi: 10.3390/cells12101359