Recurrent desmoid-type retroperitoneal fibromatosis: clinical observation
- 作者: Budurova M.1, Fainshtein I.1, Turupaev K.2, Kalinin A.1, Kozlov N.1
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隶属关系:
- Blokhin National Medical Research Center of Oncology
- Yevdokimov Moscow State University of Medicine and Dentistry
- 期: 卷 22, 编号 4 (2020)
- 页面: 125-129
- 栏目: CLINICAL ONCOLOGY
- URL: https://journals.rcsi.science/1815-1434/article/view/61191
- DOI: https://doi.org/10.26442/18151434.2020.4.200424
- ID: 61191
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This article deals with the rare clinical observation of the patient with recurrent desmoid-type fibromatosis, who have achieved long-term stability after surgical treatment. A 24-year-old patient was diagnosed with retroperitoneal tumor which size was 8.8×5.6×13 cm in 2013, infiltrating the left psoas muscle, left kidney, left common and left external iliac arteries, descending colon and sigmoid colon. The patient underwent surgery in the volume of the tumor removal, resection of the left common iliac artery and prosthetics using GORE-TEX prosthesis, left hemicolectomy, left nephrectomy at Blokhin National Medical Research Center of Oncology. The first recurrence of the tumor was detected nine months after the surgery. Due to the subsequent growth of tumor mass, located along the left external iliac artery and in the inguinal canal, the repeated surgery was performed. Then the patient had a second relapse, and underwent surgery again. The third recurrence was detected seven months after the last surgery. During the multidisciplinary discussion, according to the absence of complaints and the small size of the recurrent tumor, as well as the absence of the risk of life-threatening complications, it was decided to stop on the observation. The patient was examined once every six months – there were no data concerning recurrent tumor growth. Today, the patient is alive, does not have any complaints and is able-bodied. Our clinical observation demonstrates that active surgical tactics in case of the retroperitoneal fibromatosis recurrence not always can lead to long-term progression-free survival time and several patients can stay under the observation, using Look and Stay tactic.
作者简介
Marina Budurova
Blokhin National Medical Research Center of Oncology
编辑信件的主要联系方式.
Email: m.budurova@rambler.ru
ORCID iD: 0000-0003-1391-0516
SPIN 代码: 1412-8811
D. Sci. (Med.)
俄罗斯联邦, MoscowIgor Fainshtein
Blokhin National Medical Research Center of Oncology
Email: m.budurova@rambler.ru
ORCID iD: 0000-0002-1647-9234
D. Sci. (Med.)
俄罗斯联邦, MoscowKirill Turupaev
Yevdokimov Moscow State University of Medicine and Dentistry
Email: m.budurova@rambler.ru
ORCID iD: 0000-0001-8887-5108
Clinical Resident
俄罗斯联邦, MoscowAleksei Kalinin
Blokhin National Medical Research Center of Oncology
Email: m.budurova@rambler.ru
ORCID iD: 0000-0001-7457-3889
Cand. Sci. (Med.)
俄罗斯联邦, MoscowNikolai Kozlov
Blokhin National Medical Research Center of Oncology
Email: m.budurova@rambler.ru
ORCID iD: 0000-0003-3852-3969
Cand. Sci. (Med.)
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