Case of a congenital dystrophic violent epidermolysis


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Abstract

Clinical case of generalized form of congenital dystrophic violent epidermolysis at the patient M., 26 age is presented. The disease constantly progressed and proceeded with the classical picture expressed by all implications and symptoms characteristic of this form of illness. Despite of treatment new organs were involved in the process: kidneys, eyes, the hemopoietic system, developed a cachexia, contractures. Quality of life considerably worsened, difficulties in movements appeared. This case shows disease severity, gravity of the implications and complications leading to disability.

About the authors

V. V Dumchenko

Astrakhan State Medical University; Astrakhan Regional Skin and Venereal Diseases Dispensary

Department of deimatovenerology Astrakhan, 414000, Russian Federatoin

T. A Tkachenko

Astrakhan Regional Skin and Venereal Diseases Dispensary

Astrakhan, 414056, Russian Federatoin

E. G Bakhmutova

Astrakhan Regional Skin and Venereal Diseases Dispensary

Astrakhan, 414056, Russian Federatoin

I. V Stepanova

Astrakhan Regional Skin and Venereal Diseases Dispensary

Astrakhan, 414056, Russian Federatoin

L. P Lozovaya

Astrakhan Regional Skin and Venereal Diseases Dispensary

Astrakhan, 414056, Russian Federatoin

Lidiya N. Vetoshkina

Astrakhan State Medical University; Astrakhan Regional Skin and Venereal Diseases Dispensary

Email: lidaveto@mail.ru
MD, PhD, assistant to Department of dermatovenerology of Astrakhan State Medical University Astrakhan, 414000, Russian Federatoin

References

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