Email this article Squamous-cell cancer of the skin in pigmented xeroderma
- Authors: Albanova V.I.1
-
Affiliations:
- I.M. Setchenov First Moscow State Medical University
- Issue: Vol 17, No 6 (2014)
- Pages: 8-12
- Section: Articles
- URL: https://journals.rcsi.science/1560-9588/article/view/36894
- DOI: https://doi.org/10.17816/dv36894
- ID: 36894
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Abstract
Squamous-cell carcinoma of the skin in patients with pigmented xeroderma is characterized by early onset, aggressive course, and rapid metastatic growth. The development of malignant tumors can be prevented by early diagnosis and stringent limitation ofphotoexposure of the skin. A clinical case is presented: an 8-year-old child with multiple tumors on the face with destruction of the sublying bone and cartilage tissues and metastases in the regional lymph nodes. The first tumor emerged at the age of 4 years, dissemination started at 5. Surgery, close-focus X-ray therapy, roaccutan, and cyclophosphamide were ineffective.
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##article.viewOnOriginalSite##About the authors
Vera I. Albanova
I.M. Setchenov First Moscow State Medical University
Email: albanova@rambler.ru
MD, PhD, DSc, prof. 119991, Moscow, Russia
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