Polyostotic form of metaphyseal fibrous bone defect in children

A. I. Snetkov; Снетков А. И.; G. N. Berchenko; Берченко Г. Н.; A. K. Morozov; Морозов А. К.; S. Yu. Batrakov; Батраков С. Ю.; R. N. Pavlov; Павлов Р. Н.

doi:10.17816/vto99819

Polyostotic form of metaphyseal fibrous bone defect in children

Authors: Snetkov A.I.¹, Berchenko G.N.¹, Morozov A.K.¹, Batrakov S.Y.¹, Pavlov R.N.¹
Affiliations:
1. Central Institute of Traumatology and Orthopedics. N.N. Priorova
Issue: Vol 9, No 2 (2002)
Pages: 63-68
Section: Articles
URL: https://journals.rcsi.science/0869-8678/article/view/99819
DOI: https://doi.org/10.17816/vto99819
ID: 99819

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Abstract

Fourteen patients, 8—16 years, with polyossal form of metaphyseal fibrous bone defect (MFBD) were treated. The most rear variant of polyossal form of MFBD, i.e. Jaffe-Campanacci syndrome, was described for the first time in native literature. Two variants of pathologic focus localization, i.e. subperiosteal and intracortical, were detected by radiologic examination. Histologic pictures of mono- and polyossal forms of MFBD were identical. However, in Jaffe- Campanacci syndrome marked polymorphism of one-nucleiform cellular elements was observed. Differentiation-diagnostic signs of polyossal form of MFBD were defined. In most cases the conservative treatment was used, 3 patients were treated surgically.

Keywords

metaphyseal fibrous bone defect, tumor-like diseases of the skeleton, skin pigmentation