Treatment of a patient with mucopolysaccharidoses type II (Hunter syndrome) complicated by craniovertebral spinal canal stenosis


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Abstract

Formation of spinal canal stenosis at T12-L1 level, rarely at the level of craniovertebral junction, is a typical spinal disorder in different types of mucopolysaccharidoses that is a serious complication due to tetraparesis and tetraplegia development. Clinical, roentgenologic and therapeutic aspects of the mucopolysaccharidoses type II course in a 23 months old boy as well as the results of two-step surgical treatment for the cervical spine stabilization and elimination of spinal canal stenosis at the level of craniovertebral junction are presented.

About the authors

Luydmila K. Mikhailova

N.N. Priorov National Medical Research Center of Traumatology and Orthopaedics

Email: cito-uchsovet1@mail.com
Dr. med. sci., Professor, Consultant, Scientific and Outpatient department Moscow, Russia

A. A Kuleshov

N.N. Priorov National Medical Research Center of Traumatology and Orthopaedics

доктор мед. наук, рук. группы вертебрологии Moscow, Russia

M. S Vetrile

N.N. Priorov National Medical Research Center of Traumatology and Orthopaedics

канд. мед. наук, старший науч. сотр. группы вертебрологии Moscow, Russia

I. N Lisyanskiy

N.N. Priorov National Medical Research Center of Traumatology and Orthopaedics

канд. мед. наук, врач группы вертебрологии Moscow, Russia

O. A Polyakova

N.N. Priorov National Medical Research Center of Traumatology and Orthopaedics

врач травматолог-ортопед, аспиранты НМИЦ ТО им. Н.Н. Приорова Moscow, Russia

V. S Pereverzev

N.N. Priorov National Medical Research Center of Traumatology and Orthopaedics

врач травматолог-ортопед, аспиранты НМИЦ ТО им. Н.Н. Приорова Moscow, Russia

S. N Makarov

N.N. Priorov National Medical Research Center of Traumatology and Orthopaedics

канд. мед. наук, врач группы вертебрологии Moscow, Russia

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