Squamous-cell carcinoma in a female patient suffering from recessive dystrophic epidermolysis bullosa
- 作者: Karamova A.E.1, Chikin V.V.1, Albanova V.I.1, Smolyannikova V.A.2, Nefedova M.A.1, Monchakovskaya E.S.1
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隶属关系:
- State Research Center of Dermatovenereology and Cosmetology, Ministry of Healthcare of the Russian Federation
- I.M. Sechenov First Moscow State Medical University
- 期: 卷 92, 编号 3 (2016)
- 页面: 83-89
- 栏目: CLINICAL CASE REPORTS
- URL: https://journals.rcsi.science/0042-4609/article/view/116778
- DOI: https://doi.org/10.25208/0042-4609-2016-92-3-83-89
- ID: 116778
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详细
The article describes a case of squamous-cell carcinoma in a female patient aged 30 suffering from a rare inherited disease -recessive dystrophic epidermolysis bullosa (RDEB). RDEB is characterized by a high risk of squamous cell carcinoma in young patients. The most frequent form is a highly differentiated form of cancer characterized by an aggressive course with the early development of metastases and fast progression, which is the most frequent cause of death in RDEB patients. The described case of squamous cell carcinoma in a young female RDEB patient emphasizes the role of early tumor diagnostics.
作者简介
A. Karamova
State Research Center of Dermatovenereology and Cosmetology, Ministry of Healthcare of the Russian Federation
编辑信件的主要联系方式.
俄罗斯联邦
V. Chikin
State Research Center of Dermatovenereology and Cosmetology, Ministry of Healthcare of the Russian Federation俄罗斯联邦
V. Albanova
State Research Center of Dermatovenereology and Cosmetology, Ministry of Healthcare of the Russian Federation
Email: albanova@rambler.ru
俄罗斯联邦
V. Smolyannikova
I.M. Sechenov First Moscow State Medical University俄罗斯联邦
M. Nefedova
State Research Center of Dermatovenereology and Cosmetology, Ministry of Healthcare of the Russian Federation俄罗斯联邦
E. Monchakovskaya
State Research Center of Dermatovenereology and Cosmetology, Ministry of Healthcare of the Russian Federation俄罗斯联邦
参考
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