Chronic inflammatory demyelinating polyneuropathy with an acute onset. Clinical case

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Abstract

Chronic inflammatory demyelinating polyneuropathy (CIDP) is a heterogeneous treatable dysimmune neuropathy. The variety of clinical forms and course of the disease can be challenging for proper diagnosis and early treatment. In a quarter of cases CIDP starts acutely, mimicking Guillain–Barré syndrome. The early diagnosis is especially important regarding differences in treatment and prognosis of these conditions. In this article, we present a clinical case of acute onset CIDP with a detailed analysis of the differential diagnosis between acute and chronic immune-mediated neuropathies.

About the authors

Natalia A. Suponeva

Research Center of Neurology

Email: nasu2709@mail.ru
ORCID iD: 0000-0003-3956-6362
SPIN-code: 3223-6006

чл.-кор. РАН, д-р мед. наук, проф., рук. отд-ния нейрореабилитации и физиотерапии

Russian Federation, Moscow

Daria A. Grishina

Research Center of Neurology

Author for correspondence.
Email: dgrishina82@gmail.com
ORCID iD: 0000-0002-7924-3405

канд. мед. наук, рук. Центра заболеваний периферической нервной системы

Russian Federation

Yulia V. Ryabinkina

Research Center of Neurology

Email: ryabinkina11@mail.ru
ORCID iD: 0000-0001-8576-9983

д-р мед. наук, рук. отд-ния анестезиологии-реанимации с палатами реанимации и интенсивной терапии

Russian Federation, Moscow

Alina S. Arestova

Research Center of Neurology

Email: rizvanova.alina@gmail.com
ORCID iD: 0000-0002-9890-3552

врач-невролог

Russian Federation, Moscow

Evgeniya A. Melnik

Research Center of Neurology

Email: dgrishina82@gmail.com
ORCID iD: 0000-0001-5436-836X

врач-невролог

Russian Federation, Moscow

Taisiya A. Tumilovich

Research Center of Neurology

Email: tumilovich.taisiya@bk.ru
ORCID iD: 0000-0002-9538-9690

врач-невролог, аспирант

Russian Federation, Moscow

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2. Fig. 1. Evolution of vital capacity/predicted vital capacity and MRC sum score throughout the disease course.

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