Case of disseminated intestinal and cutaneous thromboangiitis (Kohlmeier-Degos' syndrome)

Lyudmila Nikolaevna Gasanenko; Гасаненко Людмила Николаевна; Ol'ga Vladimirovna Kapust'yan; Капустьян Ольга Владимировна; Nikolay Viktopovich Ovsyannikov; Овсянников Николай Виктopoвич; Sergey Mikhaylovich Mazhbich; Мажбич Сергей Михайлович; Eduard Aleksandrovich Kapralov; Капралов Эдуард Александрович; Natal'ya Viktorovna Bagisheva; Багишева Наталья Викторовна; Aleksey Vladimirovich Kononov; Кононов Алексей Владимирович; Aleksandr Mikhaylovich Kochetov; Кочетов Александр Михайлович; Marina Viktorovna Borisenko; Борисенко Марина Викторовна; L N Gasanenko; Gasanenko L N; O V Kapustyan; Kapustyan O V; N V Ovsyannikov; Ovsyannikov N V; S M Mazhbich; Mazhbich S M; E A Kapralov; Kapralov E A; N V Bagisheva; Bagisheva N V; A V Kononov; Kononov A V; A M Kochetov; Kochetov A M; M V Borisenko; Borisenko M V

Case of disseminated intestinal and cutaneous thromboangiitis (Kohlmeier-Degos' syndrome)

Authors: Gasanenko L.N.¹, Kapust'yan O.V.¹, Ovsyannikov N.V.¹, Mazhbich S.M.², Kapralov E.A.¹, Bagisheva N.V.¹, Kononov A.V.², Kochetov A.M.¹, Borisenko M.V.¹, Gasanenko LN¹, Kapustyan OV¹, Ovsyannikov NV¹, Mazhbich SM¹, Kapralov EA¹, Bagisheva NV¹, Kononov AV¹, Kochetov AM¹, Borisenko MV¹
Affiliations:
1. Муниципальное учреждение здравоохранения Омская городская клиническая больница № 1 им. Кабанова А. Н
2. Омская государственная медицинская академия
Issue: Vol 82, No 2 (2010)
Pages: 54-56
Section: Editorial
URL: https://journals.rcsi.science/0040-3660/article/view/30552
ID: 30552

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Abstract

Disseminated intestinal and cutaneous thromboangiitis (Kohlmeier-Degos' syndrome) is a rare syndrome of unknown etiology, which is characterized by cutaneous and visceral involvement. Two (cutaneous and visceral) stages are identified. A fatal outcome is inevitable although there may be a long (8-20-year) course of the disease during a benign process. The causes of death are peritonitis, central nervous system impairments, pleurisy, pericarditis. The paper describes a case of disseminated intestinal and cutaneous thromboangiitis (Kohlmeier-Degos' syndrome) in a 32-year-old female patient who has died from intoxication due to severely impaired permeability of the epithelial barrier mainly of the large bowel (diphtheritic inflammation of the mucosa, severe inflammatory edema of the submucous layer, and fibrinous impregnation of the serous membrane).

Keywords

thromboangiitis (Kohlmeier-Degos' syndrome), fatal intestinal and cutaneous syndrome, diagnosis, treatment

References

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Case of disseminated intestinal and cutaneous thromboangiitis (Kohlmeier-Degos' syndrome)

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