Left ventricular non - compaction: contemporary view of genetic background, clinical course, diagnostic and treatment
- 作者: Streltsova A1, Gudkova A1,2, Kostareva A1,2
-
隶属关系:
- Almazov Federal Medical Research Centre
- Pavlov First St. Petersburg State Medical University
- 期: 卷 91, 编号 12 (2019)
- 页面: 90-97
- 栏目: Editorial
- URL: https://journals.rcsi.science/0040-3660/article/view/33751
- DOI: https://doi.org/10.26442/00403660.2019.12.000142
- ID: 33751
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详细
This review highlights and discusses recent advances in understanding left ventricular non - compaction (LVNC). Clinical profile, prognosis and even diagnosis are still a great challenge faced by the world. The population prevalence of left ventricular non - compaction remains unknown. High variability of clinical manifestations, genetic heterogenity with overlap of different phenotypes, variability of hereditary patterns suggests that LVNC seems to be rather an isolated trait or a part of phenotypic expression of different cardiac diseases or complex genetic syndromes.
作者简介
A Streltsova
Almazov Federal Medical Research CentreСанкт-Петербург, Россия
A Gudkova
Almazov Federal Medical Research Centre; Pavlov First St. Petersburg State Medical UniversityСанкт-Петербург, Россия
A Kostareva
Almazov Federal Medical Research Centre; Pavlov First St. Petersburg State Medical UniversityСанкт-Петербург, Россия
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