Functional methods of amyloid cardiomyopathy diagnostic in practice and in expert centers: A review

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Abstract

The article is a set of recommendations for the interpretation of electrocardiography and echocardiography data in patients with suspected amyloidosis of the heart. Amyloid cardiomyopathy is a progressive disease characterized by a detailed picture of congestive heart failure, poor quality of life and poor prognosis. Currently, medications have appeared that can improve the prognosis in patients with amyloidosis of the heart. Therefore, raising awareness of specialists about specific instrumental signs of the disease is an important and urgent task.

About the authors

Olga N. Dzhioeva

National Research Center for Therapy and Preventive Medicine; Yevdokimov Moscow State University of Medicine and Dentistry

Author for correspondence.
Email: dzhioevaon@gmail.com
ORCID iD: 0000-0002-5384-3795

д-р мед. наук, вед. науч. сотр. отд. фундаментальных и прикладных аспектов ожирения, рук. лаб. кардиовизуализации, вегетативной регуляции и сомнологии; проф. каф. терапии и профилактической медицины

Russian Federation, Moscow; Moscow

References

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Supplementary files

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2. Fig. 1. ECG of patient with confirmed diagnosis of TTR-amyloid cardiomyopathy.

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3. Fig. 2. Assessment of parasternal access structures in positions along the long axis of the left ventricle.

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4. Fig. 3. Estimated thickness of ventricular septum from parasternal access to short axis positions.

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5. Fig. 4. Evaluation of the thickness of the free wall of the right ventricle from the subcoostal access.

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6. Fig. 5. Evaluation of longitudinal myocardial deformation of the left ventricle. In the basal anterior-distillation and lower-distillation segments, a decrease in longitudinal deformation is noted, and in apical adjacent segments this indicator is maintained.

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